Rare Pediatrics News

5 Facts you should know about

Alveolar proteinosis

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1

Individuals with Alveolar Proteinosis often experience a build-up of a lipoproteinaceous material within the alveoli, leading to impaired gas exchange in the lungs

 

2

Diagnosis typically involves imaging studies like chest X-rays or CT scans, alongside bronchoalveolar lavage (BAL) for confirmation through examination of the lavage fluid

3

Treatment options include whole lung lavage, a procedure aimed at removing the accumulated material from the lungs, along with potential use of medications like granulocyte-macrophage colony-stimulating factor (GM-CSF)

4

The cause of Alveolar Proteinosis can vary; it may result from disruptions in surfactant clearance or abnormal immune responses, though in some cases, the cause remains unknown

5

Prognosis after treatment is generally favorable, but recurrence is possible, necessitating ongoing monitoring

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